Risk factorsBy Mayo Clinic staff
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|Autosomal dominant inheritance pattern|
Genetic risk of neurofibromatosis type 2
The only known risk factor for acoustic neuroma is having a parent with the rare genetic disorder neurofibromatosis type 2, but this accounts for only a small number of cases. A hallmark characteristic of neurofibromatosis type 2 is the development of benign tumors on the balance nerves on both sides of your head, as well as on other nerves.
Neurofibromatosis type 2 (NF2) is known as an autosomal dominant disorder, meaning that the mutation can be passed on by just one parent (dominant gene). Each child of an affected parent has a 50-50 chance of inheriting it. In a few cases of NF2, another family member may not be affected, and the genetics in these cases can be complicated.
Another possible risk factor that may be associated with acoustic neuroma includes childhood exposure to low-dose radiation of the head and neck.
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