Mounier-Kuhn's syndrome (tracheobronchomegaly)

What is Mounier-Kuhn's syndrome?

- Jackie / Colorado

Answer

Mounier-Kuhn's syndrome (tracheobronchomegaly) is a rare lung disorder characterized by marked widening (dilation) of the windpipe (trachea) and sometimes the larger bronchial tubes (bronchiectasis). This impairs your ability to clear mucus from your lungs. As mucus accumulates in your lungs, it increases your risk of lung infections.

The cause of Mounier-Kuhn's syndrome isn't known. Although it may be present at birth (congenital), Mounier-Kuhn's syndrome rarely causes problems before age 20. Signs and symptoms include:

• Recurrent lung infections
• Raspy breathing
• Shortness of breath
• Productive cough

A doctor may make a diagnosis of Mounier-Kuhn's syndrome by:

• Chest X-ray
• Computerized tomography (CT) scan of the lungs

Treatment is usually directed at managing the signs and symptoms and may include:

• Quitting smoking
• Antibiotics
• Postural drainage to clear mucus from the lungs
• Lung transplant